Title

Antenatally diagnosed cloacal exstrophy variant with intravesical phallus in a twin pregnancy

UMMS Affiliation

Department of Surgery, Division of Urology; Department of Cell Biology

Date

6-2001

Document Type

Article

Subjects

*Abnormalities, Multiple; Anus, Imperforate; Bladder Exstrophy; *Diseases in Twins; Fatal Outcome; Humans; Infant, Newborn; Male; Penis

Abstract

We report a rare case of covered cloacal exstrophy variant with a hemiphallus trapped within partially closed bladder halves. The persistence of the cloacal membrane until at least 18 weeks' gestation, confirmed by antenatal ultrasound scanning, is discordant with existing theories of embryogenesis of cloacal exstrophy. The clinical presentation highlights the need for careful assessment, before and during surgery, to obtain a complete understanding of the anatomic defect before gender assignment and appropriate reconstructive efforts. A multispecialty approach and antenatal counseling are important, especially when only one fetus of twins has major birth defects.

Rights and Permissions

Citation: Urology. 2001 Jun;57(6):1178. DOI 10.1016/S0090-4295(01)01082-2

Related Resources

Link to Article in PubMed

Journal Title

Urology

PubMed ID

11377339